Systemic sclerosis (n = 19) | |
---|---|
Age, (years) | 55.2 ± 10.8 |
Sex (female), [n (%)] | 13 (68.4%) |
Disease duration, (years) | 60 ± 4.5 |
Time of follow-up examination after baseline examination, (days) | 756.6 ± 8.8 |
Time of baseline echocardiography between right heart catheter, (days) | 6.0 ± 10.4 |
Body mass index (kg/m2) | 24.0 ± 2.7 |
Arterial hypertension, [n (%)] | 4 (21.1) |
Smoker, [n (%)] | 2 (10.5) |
Raynaud’s syndrom, [n (%)] | 8 (42.1) |
Modified Rodnan Skin Score | 8.2 ± 6.5 |
Anti-centromere antibodies, [n (%)] | 4 (21.1) |
Anti-Scl-70 antibodies, [n (%)] | 7 (36.8) |
Pulmonary fibrosis, [n (%)] | 8 (42.1) |
Impaired renal function, [n (%)] | 2 (10.5) |
Invasive measurements | |
Cardiac output, (l/min) | 5.4 ± 0.7 |
Cardiac index, (l/min/m2) | 3.0 ± 0.4 |
PAP systolic, (mmHg) | 27.3 ± 4.9 |
PAP diastolic, (mmHg) | 11.2 ± 3.1 |
PAP mean, (mmHg) | 17.7 ± 3.5 |
PCWP mean, (mmHg) | 10.1 ± 3.6 |
SVR, (dyn × sec × cm-5) | 2203.3 ± 787.7 |
PVR, (dyn × sec × cm-5) | 188.3 ± 98.6 |