Variable | Non-worsening PAH children (n = 13) | Worsening PAH children (n = 12) | p |
---|---|---|---|
6MWD (m) | 416.41 ± 68.72 | 380.90 ± 104.00 | 0.341 |
SpO2 before 6MWT (%) | 86.00 ± 11.11 | 84.30 ± 7.83 | 0.689 |
SpO2 after 6MWT (%) | 77.41 ± 18.22 | 74.50 ± 11.53 | 0.667 |
WHO Functional class | 2.38 ± 0.50 | 2.50 ± 0.67 | 0.631 |
BNP0 level (pg/ml) | 30.53 ± 37.03 | 82.01 ± 74.80 | 0.039 |
PAPm (mmHg) | 61.53 ± 18.25 | 64.36 ± 17.13 | 0.701 |
TR (mmHg) | 91.23 ± 31.74 | 96.50 ± 14.05 | 0.602 |
sRV pressure (mmHg) | 98.61 ± 40.41 | 111.50 ± 14.05 | 0.297 |
Pericardial effusion | 2/13 (8 %) | 5/12 (20 %) | 0.200 |
RV-FAC (%) | 41.07 ± 15.10 | 33.08 ± 9.51 | 0.131 |
RV MPI | 0.26 (0.24,0.39) | 0.35 (0.29,0.59) | 0.129 |
TAPSE (cm) | 1.93 ± 0.59 | 1.64 ± 0.61 | 0.247 |
RV S/D ratio | 1.24 ± 0.28 | 1.36 ± 0.39 | 0.367 |
Indexed RA area (cm2) | 12.63 ± 3.33 | 15.35 ± 15.70 | 0.547 |
Tej (ms) | 280.50 ± 31.95 | 264.98 ± 29.18 | 0.219 |
LV-EI | 1.31 ± 0.17 | 1.56 ± 0.26 | 0.010 |
S’ (cm/s) | 12.83 ± 3.34 | 10.58 ± 3.50 | 0.114 |
LV-EF | 71.76 ± 11.07 | 70.58 ± 8.86 | 0.771 |
RV-LpsS (%) | |||
RV free wall | −17.38 ± 2.51 | −13.66 ± 3.24 | 0.004 |
Basal RV free wall | −12.69 ± 4.64 | −12.91 ± 4.01 | 0.899 |
Mid RV free wall | −20.76 ± 4.62 | −14.00 ± 3.13 | 0.0001 |
Apical RV free wall | −18.69 ± 4.00 | −14.08 ± 4.92 | 0.017 |
Apex | −19.15 ± 4.25 | −16.25 ± 4.37 | 0.106 |
IVS | |||
Apical IVS | −19.69 ± 5.49 | −19.00 (−22.00,−13.00) | 0.337 |
Mid IVS | −18.30 ± 4.76 | −16.33 ± 6.63 | 0.399 |
Basal IVS | NA | NA | NA |
RV-LpsSR(s −1 ) | |||
RV free wall | −1.16 ± 0.12 | −1.01 ± 0.13 | 0.008 |
Basal RV free wall | −1.00 ± 0.19 | −1.00 ± 0.09 | 0.956 |
Mid RV free wall | −1.37 ± 0.27 | −1.07 ± 0.29 | 0.013 |
Apical RV free wall | −1.11 ± 0.12 | −0.97 ± 0.16 | 0.090 |
Apex | −1.15 ± 0.19 | −1.04 ± 0.18 | 0.166 |
IVS | |||
Apical IVS | −1.21 ± 0.32 | −1.20 ± 0.20 | 0.896 |
Mid IVS | −1.17 ± 0.27 | −1.05 ± 0.34 | 0.372 |
Basal IVS | NA | NA | NA |